Image of a neural disease that would cause high-frequency hearing loss.

How often do you contemplate your nervous system? Probably not all that regularly. Usually, you wouldn’t have to worry about how your neurons are communicating signals to the nerves of your body. But you will pay more attention when something isn’t working right and the nerves begin to misfire.

There’s one specific condition, called Charcot-Marie-Tooth (CMT) disease, which can affect the nervous system on a relatively large scale, though the symptoms normally manifest chiefly in the extremities. high-frequency hearing loss can also be the result of CMT according to some research.

What Is Charcot-Marie-Tooth Disease?

Charcot-Marie-Tooth disease is a set of inherited disorders. The protective sheathing surrounding the nerves fail to function properly due to a genetic condition.

The result is that the signals sent from your brain to those nerves (and from those nerves back to your brain) don’t work all that well. A loss of motor function and sensation can be the outcome.

CMT can be found in a number of varieties and a combination of genetic considerations normally result in its expressions. Symptoms of CMT normally begin in the feet and work their way up to the arms. And, oddly, among those who have CMT, there is a higher rate of occurrence of high-frequency hearing loss.

The Cochlear Nerve: A Connection Between CMT and Hearing Loss

The connection between CMT and loss of hearing has always been colloquially recognized (that is, everyone knows someone who has a story about it – at least within the CMT culture). And it was difficult to recognize the connection between loss of sensation in the legs and issues with the ears.

A scientific study firmly established the connection just recently when a group of scientists examined 79 people with CMT at the University of Iowa Hospitals and Clinics.

The results were quite conclusive. Low to moderate frequencies were heard almost perfectly by those who had CMT. But high-frequency sounds (in the moderate region particularly) were easily heard by all of the individuals. According to this study, it seems pretty likely that CMT can at least be associated with high-frequency hearing loss.

The Cause of Hearing Loss and How to Deal With It

At first, it could be perplexing to attempt to recognize the connection between high-frequency hearing loss and CMT. Like all other parts of your body rely on properly functioning nerves. Your ears are exactly the same.

The hypothesis is, CMT impacts the cochlear nerve so noises in the high-frequency range aren’t able to be interpreted. Anybody with this type of hearing loss will have a hard time hearing certain sounds, including people’s voices. Particularly, make out voices in crowded or noisy rooms can be a real obstacle.

Hearing aids are commonly used to manage this kind of hearing loss. CMT has no known cure. Modern hearing aids can offer significant help in terms of overcoming the effects of high-frequency loss of hearing, isolating only those ranges of sounds to amplify. Most modern hearing aids can also work well in noisy settings.

There Could be Many Causes For Hearing Loss

Beyond the unconfirmed hypothesis, it’s still not well understood what the connection between CMT and high-frequency hearing loss. But hearing aid technology offers an obvious treatment for the symptoms of that loss of hearing. So scheduling an appointment to get fitted for hearing aids will be a good choice for people who suffer from CMT.

There are a range of causes for hearing loss symptoms. In some situations, hearing loss is triggered by excessive exposure to damaging noises. In other cases, hearing loss might be the result of an obstruction. It also appears that CMT is another possible cause.